中文名称: NDUFV2抗原(重组蛋白)
英文名称:NDUFV2 Antigen (Recombinant Protein)
别 名:NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa; CI-24k
储 存:冷冻(-20℃)
相关类别:抗原
概 述:Fusion protein corresponding to a region derived from 33-249 amino acids of human NDUFV2技术规格:NDUFV2抗原(重组蛋白)
Full name:
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
Synonyms:
CI-24k
Swissprot:
P19404
Gene Accession:
BC001632
Purity:
>85%, as determined by Coomassie blue stained SDS-PAGE
Expression system:
Escherichia coli
Tags:
His tag C-Terminus, GST tag N-Terminus
Background:
The NADH-ubiquinone oxidoreductase complex (complex I) of the mitochondrial respiratory chain catalyzes the transfer of electrons from NADH to ubiquinone, and consists of at least 43 subunits. The complex is located in the inner mitochondrial membrane. This gene encodes the 24 kDa subunit of complex I, and is involved in electron transfer. Mutations in this gene are implicated in Parkinson's disease, bipolar disorder, schizophrenia, and have been found in one case of early onset hypertrophic cardiomyopathy and encephalopathy. A non-transcribed pseudogene of this locus is found on chromosome 19.
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